A Case of Medallion-Like Dermal Dendrocyte Hamartoma with a Distinctive Size and Vascular Component Büyük Çaplı ve Belirgin Vasküler Komponentli Madalyon Benzeri Dermal Dendrositik Hamartoma

نویسندگان

  • Didem Dinçer
  • Mehmet Gamsızkan
  • Erol Koç
  • Özay Gököz
چکیده

DOI: 10.4328/JCAM.688 Received: 29.04.2011 Accepted: 17.05.2011 Printed: 01.07.2013 J Clin Anal Med 2013;4(4): 329-31 Corresponding Author: Mehmet Gamsızkan, Ankara Mevki Asker Hastanesi, Patoloji Laboratuarı, 06111 Dışkapı, Ankara, Turkey. T.: +90 3123103535 F.: +90 3123114609 E-Mail: [email protected] Özet Madolyon benzeri dermal dendrosit hamartom yeni tanımlanmış, oldukça nadir konjenital bir lezyondur. Lezyon, karakteristik olarak asemptomatik, iyi sınırlı, kırmızı-kahve renkte, atrofik madalyon şeklinde bir yama olup gövde üst yüz ve/ veya boyunda gözlenir. Yüzeyi yumuşak ve kırışıktır. Ayrıca, altındaki damarlar ve telenjektaziler gözlenebilir. Histopatolojik bulguları, epidermal atrofi, CD34+ iğsi hücrelerin dermal proliferasyonu ile karakterizedir. Bu zamana kadar İngilizce literatürlerde sadece 9 olgu bildirilmiştir. Bizim olgumuz daha önce bildirilen olgularla benzer özellik göstermekle birlikte diğer olgulardan daha büyük olması ve daha belirgin vasküler komponente sahip olmasıyla farklılık göstermektedir.

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تاریخ انتشار 2012